Hughes-Stovin Syndrome : A Case Report and Review of the Literature

PRATHEEP RIANTAWAN, M.D., M.Sc., M.R.C.P.(UK)*, CHAIVUD YODTASURODOM, M.D.**, TAWEESAK CHOTIVATANAPONG, M.D.**, PONGLADA SUBHANNACHART,M.D.***

Affiliation : * Division of Medicine. ** Division of Surgery, *** Division of Radiology, Central Chest Hospital, 39 Tiwanon Road. Nonthaburi 11000, Thailand.

AbstractA young man presented with prolonged pyrexia, recurrent optic neuritis, thrombophlebitis and bilateral pulmonary artery aneurysms with thrombus formation. The life-threatening hemoptysis necessitated mechanical ventilatory support and emergency left lower lobectomy. Systemic corticosteroids conferred clinical improvement and reduction of the remaining right pulmonary artery aneurysm. The patient eventually succumbed to sudden massive hemoptysis. This report underscores the unpredictable nature of this syndrome and emphasises the need for aggressive surgical intervention of pulmonary artery aneurysms in Hughes-Stovin syndrome.

Keywords : Hughes-Stovin Syndrome, Pulmonary Artery Aneurysm, Optic Neuritis

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