Syndrome of Progressive Ataxia and Palatal Myoclonus : A Case Report

KAMMANT PHANTHUMCHINDA, M.D.*

Affiliation : * Division of Neurology, Department of Medicine, Faculty of Medicine, Chulalongkom University, Bangkok 10330. Thailand.

AbstractA 46-year old man presented with progressive ~rebellar ataxia for 5 years. Physical examination revealed palatal and tongue myoclonus, cerebellar gait, limb ataxia and spasticity of the lower extremities. The imaging studies including CT-scan and MRI of the brain-revcalea progressive pancerebellar atrophy and bilateral hypertrophic degeneration of inferior olives. The clinical course was slowly progressive. Various medications included anticonvulsants, benzo- diazepines and antispasticity failed to abolish the abnormal palatal movement and ataxic syn- drome. The syndrome of progressive ataxia and palatal myoclonus is a rare and unique ncuro- degenerative syndrome. The pathogenesis and treatment are still unknown.

Keywords : Palatal Tremor, Palatal Myoclonus, Cerebellar Ataxia

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