Ileal Atresia and Total Colonic Aganglionosis

SURASAK SANGKHATHAT, M.D.*, SAKDA PATRAPINYOKUL, M.D.*, NARA DONSAKUL, M.D.**

Affiliation : * Pediatric Surgery Unit, ** Plastic & Reconstructive Surgery Unit, Department of Surgery, Faculty of Medicine, Prince of Songkla University, Songkhla, 90110, Thailand.

AbstractHerein, the authors report a case of ileal atresia who failed to have good bowel function after primary anastomosis. After the leakage of the revised anastomosis, a thorough pathological review found distal aganglionosis. An ileostomy followed by an ileocolic patch operation were per formed for temporary decompression, awaiting intestinal adaptation. A definitive pull-through was performed, eight months later. The child also had bilateral cleft lip together with complete cleft palate, and hemivertebrae of the thoracic spines. A cluster of malformations is unusual in a single patient.

Keywords : Ileal Atresia, Total Colonic Aganglionosis, Multiple Congenital Anomalies

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