Congenital Localized Multiple Fibromatosis: A Case Report
PITI PALUNGWACHIRA, M.D.*, KUNIO IW AHARA, M.D.**, MASAKO SHIRAI, M.D.**, HIDEOKI OGAWA, M.D.**
Affiliation : * Srinakharinwirot Skin Center. Srinakharinwirot University. Bangkok 10110. Thailand. ** Department of Dermatology. Juntendo University School of Medicine. 1-1. Hongo 2-Chome, Bunkyo-ku. Tokyo 113 Japan.
Abstract Clinical, histopathologic and electronmicroscopic findings in a case of congenital localized multiple fibromatosis of interscapular region are presented. This 10 year-old Japanese girl developed this lesion since she was 3 weeks old, metastases have never been observed. The histological and electron-microscopic features point to the hamartomous origin of this tumor with partial differentiation of its cells towards myofibroblasts and atypical fibroblasts. The differen- tial diagnosis from other soft tissue tumors in infancy and early childhood is discussed.
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