Cutis marmorata telangiectatica congenita (CMTC) is a sporadic congenital vascular anomaly usually presents at birth as a localized or generalized reticulated, erythema and telangiectasia. The pathogenesis of CMTC is unknown. Additional anomalies have been frequently reported in association with CMTC. This article describes the characteristics of the clinical presentations in a series of 7 children with CMTC in HRH Princess Maha Chakri Sirindhorn Medical Center, Srinakharinwirot University, Thailand. Both genders were almost equally affected (3 male/4 female). The lower limbs were involved in 7 patients (100%), the trunk in 3 patients (42.9%), and the upper limbs in 1 patient (14.3%). There were 2 patients (28.6%) who presented with the involvement of both trunk and limbs. The mean of the body surface area involved was 17% (2-50). Asymmetry of affected limbs were found in 2 patients (28.6%). On follow-up, improvement of reticulated lesions was noted in all patients. The prognosis of uncomplicated cases is good. No specific treatment is needed. The skin lesions usually disappear gradually.

Keywords: Cutis marmorata telangiectatica congenita, Benign vascular anomaly